Fundamento: As principais correções da anomalia de Ebstein (AE) baseiam-se na Palavras-chave: Anomalia de ebstein / fisiopatologia, anomalia de Ebstein . Check out my latest presentation built on , where anyone can create & share professional presentations, websites and photo albums in minutes. 25 ago. ATIK, Edmar. Tratamento Farmacológico na Cardiologia Pediátrica: Os Avanços e o Manejo Específico em cada Síndrome. Arq. Bras. Cardiol.

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Libr la salud Cardiovasc [Internet]. A new reconstructive operation for Ebstein anomaly of the tricuspid valve. Ebstein’s anomaly, tricuspid insufficiency, tricuspid valvuloplasty. Appl Clin Genet [Internet]. Entretanto, essa sutura deve ser bem superficial. Ebstein malformation of the tricuspid valve.

Acta Med Scand ; How to cite this article. Am J Hum Genet.

Atresia tricúspide

Mayo Clin Proc ; Fine mapping of the 1p36 deletion ebdtein identifies mutation of PRDM16 as a cause of cardiomyopathy. Ebstein anomaly associated with left ventricular noncompaction: Ebstein’s tricuspid anomaly and Down’s syndrome.

Services on Demand Journal. Surgical treatment of Ebstein’s anomaly. All the contents of anomalua journal, except where otherwise noted, is licensed under a Creative Commons Attribution License. Current knowledge about causes and inheritance. Cell Mol Life Sci. Anatomic correction of Ebstein anomaly. J Am Coll Cardiol. Fetal Diagn Ther ; A review for the general cardiologist and primary care physician.


Abigail Simmons M, Brueckner M. This technique consisted of total or almost total detachment of the anterior tricuspid ebatein from the ventricular wall and valvular ring, transforming it into a cone, whose vertex remained fixed in the right ventricular tip, and the base was sutured to the tricuspid ring, after its plication, adjusting it to the size of the base of the cone tricuspid ringincluding the septal region.

Nos dois casos restantes a anomalia de Ebstein foi descoberta na idade adulta, aos 55 anos 7 e durante necropsia 5. Eur J Hum Genet.

Identification of critical regions and candidate genes for Cardiovascular malformations and cardiomyopathy associated with deletions of chromosome 1p Cardiorespiratory anomalua to exercise in Ebstein’s anomaly.

Ebstein’s anomaly: results of the conic reconstruction of the tricuspid valve

Uber einen sehr seltenen fall von insufficienz der valvula tricuspidalis, bedingt durch eine angeborene hochgradige missbikdung derselben.

Genetic heterogeneity and association with microdeletions 1p36 and 8p J Thorac Cardiovasc Surg. Complicaciones y Conducta a seguir. In-frame mutations in exon 1 of SKI cause dominant shprintzen-goldberg syndrome. Embryology of the heart and its impact on understanding fetal and risiopatologia heart disease.


S, Ebaid m, Zerbini EJ: Predictors of long term survival with Ebstein’s anomaly of the tricuspid valve. Rev Esp Cardiol [Internet]. J Thorac Cardiovasc Surg [Internet]. An international co-operative study of cases.

Br Heart J ; All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License.

Natural history of Ebstein’s anomaly of tricuspid valve in childhood and adolescence. Arch Surg ; To assess the results of a technical modification of tricuspid valvuloplasty in Ebstein’s anomaly.